First reported: Sjogren's syndrome coexists with such conditions, and this test is key to diagnosis

*For medical professionals only

First case report of pediatric Sjogren syndrome with aortic arteritis

Sjögren's Syndrome (SS) is a diffuse connective tissue disease

■ The first stage: diagnosis of SS

▎ Case information A 9-year-old girl was diagnosed with cervical lymphadenitis due to "fever and cervical lymphadenopathy", and although the symptoms were relieved after treatment with antibacterial drugs, blood tests showed that the inflammatory markers continued to rise, and was referred to our hospital for further examination and treatment

■ Phase II: TAK was discovered after a five-year follow-up

• Persistently elevated inflammatory markers, occasionally found "macaroni signs"

Table 1 2016 ACR/EULAR primary SS classification criteria

*Inclusion criteria and exclusion criteria, and the sum of the following 5 scores≥ 4 points

Serological testing of autoantibodies such as ANA, RF, anti-SSA/Ro antibodies, or anti-SSB/La antibodies is a major factor

[2]omiita M,Saito K,Kohno Y,Shimojo N,Fujikawa S,Niimi H.
The clinical features of Sjögren's syndrome in Japanese children.
Acta Paediatr Jpn.
1997; 39(2):268-272.
doi:10.
1111/j.
1442-200x.
1997.
tb03597.
x

[3] Misra DP,Aggarwal A,Lawrence A,Agarwal V,Misra R.
Pediatric-onset Takayasu's arteritis:clinical features and short-term outcome.
Rheumatol Int.
2015; 35(10):1701-1706.
doi:10.
1007/s00296-015-3272-7

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This article is from | Medical community rheumatic immunity channel

This article is written by | Zhou Zhici

This article is reviewed | Chen Xinpeng Deputy Chief Physician

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